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Interseksnist abo Interseksua lnist zagalnij termin dlya poznachennya grupi staniv pri yakih rozdilnostatevij organizm maye statevi oznaki sho ne mozhut buti chitko viznacheni yak cholovichi abo zhinochi 1 Interseks osobi lyudi sho narodilisya z takimi variantami statevih oznak hromosominij nabir vnutrishni ta zovnishni statevi organi statevi gormoni tosho yaki vidpovidno do Upravlinnya Verhovnogo komisara OON z prav lyudini ne pidhodyat pid tipovi viznachennya dlya cholovikiv abo zhinok 2 Interseksualnist mozhe buti ochevidnoyu pri narodzhenni statevi organi mozhut buti neodnoznachnimi i viglyadati yak promizhnij variant mizh cholovichimi ta zhinochimi 3 4 Z 2015 roku Vsesvitnya organizaciya ohoroni zdorov ya ta OON pochali vivoditi interseksualnist z ploshini patologiyi statevogo rozvitku ta predstavlyati ce yak variaciyu statevogo rozvitku 5 nini nayavnist interseksualnih ris ne vvazhayetsya hvoroboyu 4 Interseksualnist ne varto plutati z ginandromorfizmom yakij virazheno sposterigayetsya perevazhno u chlenistonogih i takozh zustrichayetsya u ptahiv Pri ginadromorfizmi odni chastini tila mayut cholovichi risi a inshi zhinochi mozhlivij navit variant bilateralnoyi asimetriyi koli odna polovina tila maye cholovichu budovu a insha zhinochu 6 7 8 Prapor Interseks lyudejNa dumku ekspertiv priblizno vid 0 05 do 1 7 naselennya narodzhuyetsya z interseksnimi oznakami 9 10 Zmist 1 Terminologiya 2 Oznaki 3 Interseksualni stani ta prichini yih rozvitku 3 1 46 XX interseks 3 2 46 XY interseks 3 3 Spravzhnij gonadalnij interseks 3 4 Skladnij abo neviznachenij interseks 4 Medichne vtruchannya 4 1 Tipi medichnogo vtruchannya 5 Prichini 5 1 Zigotna genetichno obumovlena interseksnist 5 2 Gormonna interseksnist 6 Interseks ta prava lyudini 7 Zahist vid diskriminaciyi 7 1 Pracevlashtuvannya 7 2 Ohorona zdorov ya 7 3 Sport 8 Div takozh 9 Posilannya 10 Literatura 11 PrimitkiTerminologiya RedaguvatiTermin interseksualnist buv vvedenij Richardom Goldshmidtom 1917 roku 11 Interseks lyudej ranishe nazivali germafroditami 12 U XIX XX stolitti bula zdijsnena persha sproba stvoriti klasifikaciyu interseksualnih staniv Yih podilili na spravzhnij germafroditizm zhinochij psevdogermafroditizm ta cholovichij psevdogermafroditizm 13 Nini ci termini ye zastarilimi a slovo germafrodit ne mozhe vzhivatisya stosovno lyudini 14 lishe stosovno tvarini abo roslini sho mayut yak cholovichi tak i zhinochi reproduktivni organi 13 Z 2006 roku u medicini vzhivayut termin porushennya statevogo rozvitku DSD 15 yaka ohoplyuye vrodzheni stani pri yakih rozvitok hromosomnoyi gonadnoyi abo anatomichnoyi stati ye netipovim 16 ale i sam DSD oskarzhuyetsya gromadskimi organizaciyami pravozahisnimi institutami ta naukovcyami U travni 2016 roku Interact Advocates for Intersex Youth opublikuvav zayavu proti patologizuyuchoyi movi dlya opisu lyudej narodzhenih z interseksualnimi risami viznayuchi posilennya zagalnogo rozuminnya ta prijnyattya termina interseks 17 Deyaki lyudi z interseksnimi risami samoidentifikuyutsya yak interseks osobi a deyaki ni 18 19 Avstralijske sociologichne doslidzhennya opublikovane 2016 roku pokazalo sho 60 respondentiv vikoristovuvali termin interseks shob opisati svoyi statevi harakteristiki Bilshist takozh opisuyut sebe yak cholovik abo zhinka 20 Oznaki Redaguvati nbsp Voskovij maket genitalij 46 XY interseks lyudiniHocha mi govorimo pro interseks yak vrodzhenij stan interseks anatomiya ne zavzhdi proyavlyayetsya pri narodzhenni Inodi interseksnist mozhe buti viyavlena lishe pri dosyagnenni statevogo dozrivannya abo navit u dorosloyi lyudini mozhlive j viyavlennya vzhe pislya smerti lyudini za dopomogoyu autopsiyi U deyakih lyudej interseksnist ne viyavlyayut uzagali 1 Proyavi interseksnosti zalezhat vid yiyi prichini 21 Inodi zovnishni statevi organi mozhut viglyadati yak tipovi cholovichi abo zhinochi 1 Viyavlennya pri narodzhenni mozhlive yaksho genitaliyi nemovlyati ne mozhut buti odnoznachno viznachenimi yak cholovichi abo zhinochi 4 Ce mozhe viyavlyatisya u Zbilshenomu klitori megaklitoremiya 21 4 Zmenshenomu penisi mikropenis 21 4 Vidsutnosi vaginalnogo otvoru 4 Gipospadiyi otvir uretri znahoditsya ne na kinci penisa 21 4 Zakritih statevih gubah sho nagaduyut kalitku moshonku 4 Vidkritij moshonci sho nagaduye statevi gubi 4 Takozh v interseks lyudej mozhe buti zatrimka statevogo dozrivannya anomaliyi elektrolitiv a pri deyakih stanah nespodivani zmini pid chas statevogo dozrivannya 21 Koli narodzhuyetsya malyuk zazvichaj likari viznachayut jogo stat spirayuchis na pevnu shkalu Tak shkala yaku v 1995 roci rozrobiv likar endokrinolog Charmian Kuigli maye sim stupeniv de pershij stupin virazna maskulinnist tobto yavno virazheni cholovichi statevi organi a somij virazno feminni statevi proyavi tobto zhinochi Stat viznachena za ciyeyu shkaloyu nazivayetsya akusherskoyu stattyu 5 nbsp Interseksualni stani ta prichini yih rozvitku RedaguvatiInterseks stani mozhna rozdiliti na 4 kategoriyi 46 XX interseks 46 XY interseks Spravzhnij gonadalnij interseks Skladnij abo neviznachenij interseks 21 46 XX interseks Redaguvati Vinikaye yaksho pid chas pershogo trimestru vagitnostina plid sho maye zhinochij genotip diyut veliki dozi androgeniv Ci androgeni mozhut mati yak ekzogenne tak i endogenne pohodzhennya Nadmirna kilkist ekzogennih androgeniv sho vplivaye na rozvitok ploda vinikaye vnaslidok prijomu matir yu anabolichnih steroyidiv nayavnosti v neyi androgen produkuyuchih puhlin nadnirnikiv chi yayechnikiv abo nayavnosti v materi vrodzhenoyi giperplaziyi nadnirkovih zaloz Prichinoyu nadlishku endogennih androgeniv mozhe buti vrodzhena giperplaziya nadnirkovih zaloz u samogo ploda Vrodzhena giperplaziya nadnirkovih zaloz vinikaye vnaslidok spadkovogo defektu odnogo z fermentiv neobhidnih dlya virobnictva kortizolu deficit 21 gidroksilazi deficit 11 beta gidroksilazi deficit 3 beta gidroksisteroyiddegidrogenazi vnaslidok chogo produkuyetsya nadmirna kilkist androgeniv dlya kompensaciyi nestachi kortizolu U nemovlyat zhinochoyi stati ce prizvodit do maskulinizaciyi z anomalnim rozvitkom statevih organiv todi yak u nemovlyat cholovichoyi stati do peredchasnogo statevogo rozvitku Krim togo prichinoyu mozhe buti deficit aromatazi placenti R450 sho prizvodit do nadlishkovoyi produkciyi androgeniv placentoyu 22 23 24 Vrodzhena giperplaziya nadnirkovih zaloz traplyayetsya v odnomu vipadku z 50 1000 narodzhen 0 1 0 2 do 1 2 zalezhno vid naselennya 25 Takim chinom pri vrodzhenij giperplaziyi nadnirkovih zaloz lyudina maye tipovi dlya zhinok statevi hromosomi ta gonadi ale zovnishni statevi organi nagaduyut cholovichi statevi gubi zrostayutsya a klitor zbilshuyetsya Matka i matkovi trubi pri comu zazvichaj v normi Ranishe ce yavishe nazivali zhinochim psevdogermafroditizmom 21 Maskulinizuyuchij efekt trivaye i pislya narodzhennya tomu lyudina mozhe mati guste volossya na tili glibokij golos tosho Mozhlive takozh porushennya balansu natriyu v sirovatci krovi U osib z XY vrodzhena giperplaziya nadnirkovih zaloz ne prizvodit do rozvitku interseksnih ris ale mozhe prizvesti do priskorenogo statevogo dozrivannya 26 46 XY interseks Redaguvati nbsp Model Hanna Gabi Odil Maye sindrom nechutlivosti do androgeniv Ranishe poznachavsya terminom cholovichij psevdogermafroditizm U cih lyudej zazvichaj rozvivayutsya normalni yayechka ale maskulinizaciya sistemi volfovih protok ta zovnishnih statevih organiv ye nepovnoyu Chasto osobi narodzhuyutsya z neviznachenistyu genitalij yayechka mozhut buti zokrema vnutrishnocherevnimi chi tazovimi Mozhut rozvivatisya molochni zalozi mozhliva nayavnist klitora ta malorozvinenoyi vagini 27 28 29 30 Prichini mozhut polyagati u znizhenij produkciyi testosteronu vnaslidok porushennya aktivnosti chi gipoplaziyi klitin Lejdiga abo defektu receptora do lyuteyinizuyuchogo gormonu na nih porushennya biosintezu testosteronu pri defektah 20 22 desmolazi 3 beta gidroksisteroyiddegidrogenazi 17 20 gidroksilazi 17 beta gidroksisteroyiddegidrogenazi sho berut uchast u steroyidogenezi v nadnirnikah Chastoyu prichinoyu rozvitku cogo stanu ye nechutlivist do androgeniv Krim togo cej stan mozhe zumovlyuvatisya defektami rozvitku yayechok takimi yak XY disgeneziya gonad zmishanij disgenez gonad i sindromi rudimentarnogo yayechka 31 Okrim togo porushennya maskulinizaciyi mozhe viklikatisya deficitom 5a reduktazi Deficit 5a reduktazi ce interseksnij stan sho sprichinenij autosomno recisivnoyu mutaciyeyu u geni SRD5A2 sho koduye 5a reduktazu tipu 2 32 Cej ferment vidpovidaye za peretvorennya testosteronu v digidrotestosteron sho ye fiziologichno aktivnishim i ye neobhidnim dlya normalnogo rozvitku cholovichih zovnishnih statevih organiv plodu 33 Tomu lyudi z deficitom cogo fermentu narodzhuyutsya z genitaliyami duzhe podibnimi do zhinochih Ale pid chas statevogo dozrivannya riven cholovichih statevih gormoniv u cih osib pidvishuyetsya sho prizvodit do rozvitku vtorinnih statevih oznak roste m yazova masa pogliblyuyetsya golos pochinaye zbilshuvatisya yih klitoropodibnij penis pri comu ovolosinnya oblichchya v nih chasto ne virazhene Bagato z nih vihovuyutsya yak divchatka 34 35 Sindrom nechutlivosti do androgenivSindrom nechutlivosti do androgeniv Sindrom Morrisa ce genetichnij defekt roztashovanij v H hromosomi yakij mozhe buti uspadkovanim abo vinikati za rahunok spontannih mutacij Sindrom Morrisa zustrichayetsya priblizno u odniyeyi osobi iz 20000 Klitini lyudej z cim sindromom povnistyu abo chastkovo ne zdatni reaguvati na androgeni sho prizvodit do rozvitku statevih organiv za zhinochim tipom U plodu ne formuyutsya matka matkovi trubi ta verhnya chastina pihvi ale zovnishni statevi organi viglyadayut podibnimi do zhinochih vidsutni takozh pridatki yayechka sim yavividni protoki ta sim yani puhirci Yayechka opusheni abo chastkovo opusheni vagina yak pravilo korotka bez shijki matki Inodi pihva majzhe vidsutnya Ci lyudi ne mayut menstruacij i ye nefertilnimi chasto v nih takozh ne roste volossya pid pahvami i na lobku grudi zazvichaj rostut ale inodi piznishe nizh u bilshosti zhinok Pri viyavlenni cogo sindromu rekomenduyetsya vidalennya yayechok oskilki ye visokij rizik rozvitku raku ale oskilki ce ridko vidbuvayetsya do statevogo dozrivannya chasto rekomenduyetsya pochekati do togo viku v yakomu lyudina sama zmozhe prijnyati ce rishennya 36 Spravzhnij gonadalnij interseks Redaguvati Zastarila nazva spravzhnij germafroditizm Spravzhnij gonadalnij interseks ovotestikulyarnij rozlad 37 38 39 interseksualnij stan pri yakomu v mezhah odnogo organizmu viyavlyayutsya yak folikuli yayechnikiv tak i sim yani kanalci sho mozhut buti prisutnimi yak v riznih gonadah tak i v mezhah odniyeyi Gonada v yakij znahodyatsya i tkanini yayechnikiv i yayechok nazivayetsya ovotestisom tkanini yayechka v ovotestisi zazvichaj zajmayut centralne polozhennya a tkanini yayechnika roztashovani na periferiyi 40 41 33 U 90 vipadkiv pochatkovim proyavom spravzhnogo gonadalnogo interseksu ye neodnoznachnist genitalij hocha v ridshih vipadkah zustrichayutsya genitaliyi yaki harakterni dlya zhinochoyi chi cholovichoyi stati a stupin neodnoznachnosti zalezhit v osnovnomu vid kilkosti testosteronu sho viroblyayetsya tkaninoyu yayechka mizh 8 i 16 tizhnem vagitnosti Poshirenoyu ye nayavnist labioskrotalnih skladok Chasto traplyayetsya pahova grizha Roztashuvannya gonad odna vidnosno odnoyi buvaye bilateralnim dvostoronnim koli nayavni lishe ovotestisi sho rozmisheni po bokah 30 unilateralnim odnostoronnim koli z odnogo boku ovotestis a kolateralno do nogo znahoditsya normalnij yayechnik 50 abo sim yanik lateralnim koli z odnogo boku yayechko a z inshogo yayechnik 20 Pri comu yayechniki chastishe roztashovuyutsya zliva 76 5 a ovotestisi i yayechka sprava 60 3 Sami ovotestisi mozhut zajmati cherevne 50 pahove 26 ta labioskrotalne 24 polozhennya Priblizno u 75 osib zustrichayetsya ginekomastiya she dlya priblizno 50 osib harakterna menstruaciya pri comu u tih interseks osib sho mayut penis menstruaciya yavlyaye soboyu ciklichnu gematuriyu Bilshist lyudej z cim interseksnim stanom maye matkovij rig abo matku 90 matka chasto normalno rozvinena takozh poshirenoyu ye nayavnist urogenitalnogo sinusa Tkanina yayechnikiv yak pravilo normalna a tkanina yayechok najchastishe ye disgenetichnoyu i spermatogenez v nij zustrichayetsya vkraj ridko Dvi tretini osib z ovotestikulyarnim rozladom vihovuyutsya yak choloviki Vagitnist mozhliva 41 42 43 44 45 46 Vipadki narodzhuvanosti u lyudej z cim stanom vkraj ridkisni 47 48 Ci osobi zazvichaj mayut funkcionalnu tkaninu yayechnikiv ye dani sho 50 lyudej z ovotestisami mozhut projti ovulyaciyu ale yih sim yani zalozi nedostatno rozvineni tomu spermatogenez duzhe ridkisnij 49 50 10 30 osib mayut gen SRY ale u bilshosti 60 70 kariotip 46 HH i voni mayut sim yani kanalci popri vidsutnist SRY otzhe u nih vidbuvayetsya aktivaciya genu sho v normi aktivuyetsya SRY Takozh poshireni rizni formi mozayichnosti 20 41 V cilomu zustrichayutsya taki kariotipi 46XX 46XY abo 46XX 47XXY abo XX amp XY z mutaciyami SRY zmishanimi hromosomnimi anomaliyami abo z gormonalnimi porushennyami 47XXY ta riznimi stupenyami mozayichnosti cih ta bagatoh kariotipiv 3 osnovni kariotipi spravzhnogo germafroditizmu XX z genetichnimi anomaliyami 55 70 vipadkiv XX XY 20 30 vipadkiv ta XY 5 15 vipadkiv U medichnij literaturi zafiksovano lishe 500 vipadkiv 50 Skladnij abo neviznachenij interseks Redaguvati Bagato konfiguracij hromosom krim prostih 46 XX abo 46 XY mozhut prizvesti do poyavi interseksnih ris Zokrema 45 XO Sindrom Ternera i 47 XXY Sindrom Klyajnfeltera tosho Ci rozladi ne prizvodyat do nevidpovidnosti mizh zovnishnimi ta vnutrishnimi statevimi organami ale vplivayut na rozvitok statevih oznak 21 Tak u zhinok z sindromom Ternera feminni oznaki mensh virazheni nizh u bilshosti zhinok 51 voni duzhe chasto ye bezplidnimi 52 a pri vagitnosti rizik vikidnya chi poyavi defektiv rozvitku ye vishim nizh u bilshosti zhinok 53 U osib z sindromom Klyajnfeltera mensh virazhenimi ye maskulinni risi napriklad yayechka zazvichaj ye znachno menshimi nizh u bilshosti cholovikiv Cej sindrom traplyayetsya priblizno v odnogo hlopchika z 500 1 000 narodzhenih 54 Ci lyudi mayut odnu abo bilshe zajvih H hromosom i zazvichaj ye bezplidnimi 55 Traplyayetsya zmenshennya ovolosinnya slabkist m yaziv zmenshennya statevih organiv tosho 56 Takozh mozhlivi rizni mozayicizmi zokrema pri sindromi Ternera ta Klyajnfeltera Lyudina z mozayichnim fenotipom maye riznij kariotip v riznih klitinah napriklad chastina klitin mozhe mati normalnij kariotip a chastina trisomiyu 47 XXX 46 XX chi monosomiyu 45 X0 46 XX 57 Medichne vtruchannya Redaguvati nbsp Krayini v yakih diye zaborona na medichni vtruchannya bez zgodiMedichni vtruchannya provodyatsya dlya pokrashennya fizichnogo zdorov ya ta zmenshennya psihosocialnih rizikiv ale obidvi ci prichini ye predmetom diskusij osoblivo vrahovuyuchi te sho naslidki hirurgichnih ta deyakih gormonalnih vtruchan ye nezvorotnimi todi yak yih docilnist daleko ne zavzhdi ye ochevidnoyu Ne isnuye klinichnogo konsensusu shodo togo v yakih vipadkah hirurgichne vtruchannya ye neobhidnimi yakim vono maye buti i koli povinne provoditisya 58 59 60 Taki operaciyi ye predmetom suttyevih superechok cherez svoyi naslidki taki yak travmi vpliv na statevi funkciyi porushennya prav na fizichnu ta psihichnu cilisnist 61 Medichni vtruchannya bez zgodi na zminu statevih harakteristik interseks lyudej provodyatsya u vsih krayinah de doslidzhuvalis prava interseksnih lyudej 62 Taki zahodi kritikuyutsya Vsesvitnoyu organizaciyeyu ohoroni zdorov ya ta inshimi organami OON takimi yak Upravlinnya Verhovnogo komisara z prav lyudini ta dedali bilshoyu kilkistyu regionalnih ta nacionalnih ustanov U krayinah z nizkim ta serednim rivnem dohodu vartist medichnogo obslugovuvannya mozhe obmezhuvati dostup do neobhidnogo medichnogo likuvannya odnochasno z tim sho inshi osobi otrimuyut primusovi medichni vtruchannya 63 Zaznacheno sho mozhut porushuvatisya taki prava nepovnolitnih interseks osib pravo na zhittya 64 pravo na privatne zhittya vklyuchayuchi pravo na osobistu avtonomiyu chi samoviznachennya shodo likuvannya 65 66 zaboroni katuvan ta inshogo zhorstokogo ta takogo sho prinizhuye gidnist povodzhennya 67 pravo na fizichnu nedotorkannist ta abo tilesnu avtonomiyu 68 69 Tipi medichnogo vtruchannya Redaguvati Feminizuyuchi ta maskulinizuyuchi operaciyi Yak pravilo operaciya provoditsya nezabarom pislya narodzhennya Zahisniki ciyeyi praktiki stverdzhuyut sho dlya togo shob interseks lyudi mogli funkcionuvati socialno ta rozvivatisya normalno neobhidno chitko viznachiti lyudej yak cholovikiv chi zhinok Chasto zaznachayutsya psihosocialni prichini 70 Ale cya praktika kritikuyetsya bagatma pravozahisnimi ustanovami ta avtorami oskilki operaciya na statevih organah mozhe prizvesti do negativnih naslidkiv dlya statevogo funkcionuvannya v podalshomu zhitti abo do pochuttya chudernackosti ta neprijnyatnosti 71 Bagatom interseks dityam roblyat operaciyi namagayuchis normalizuvati yih hocha ci vtruchannya chasto invazivni nezvorotni ta ne ye neobhidnimi chi nevidkladnimi Doslidzhennya Amnesty International pokazali sho taki medichni vtruchannya ye porushennyam prav lyudini Chasto yih provodyat dityam yaki cherez vik ne mozhut brati uchast v uhvalenni rishen shodo vlasnogo tila a yihni batki chasto ne nalezhnim chinom informovani pro mozhlivi riziki Proceduri provedeni interseks dityam mozhut sprichinyati veliki problemi vklyuchno z bezpliddyam bolem netrimannyam sechi ta psihologichnim strazhdannyam protyagom usogo yihnogo zhittya 9 Takimi operaciyami mozhut buti zmenshennya abo repoziciya klitora inodi jogo nazivayut klitoroplastikoyu vaginoplastika vidnovlennya gipospadiyi gonadektomiya Bilshist takih operacij robitsya dityam do dvoh rokiv takim chinom yim vidmovlyayut u vibori yakij mozhe serjozno vplinuti na fertilnist statevi funkciyi ta emocijnij dobrobut U zviti opublikovanomu u Journal of Pediatric Urology 2016 roku pokazano sho 35 iz 37 batkiv interseks ditej obrali kosmetichnu hirurgiyu na svoyih dityah 72 Gormonalne likuvannya Gormonalne likuvannya poshirene dlya zapobigannya viniknennyu abo dlya usunennya interseksnih ris 73 Psihosocialna pidtrimka nbsp Uchasniki tretogo Mizhnarodnogo forumu Interseks lyudej Malta gruden 2013 roku Cya praktika zazvichaj pidtrimuyetsya zacikavlenimi storonami tak u spilnij zayavi uchasnikiv tretogo Mizhnarodnogo forumu Interseks lyudej vimagalosya viznannya togo sho medikalizaciya ta stigmatizaciya interseks lyudej ye travmatizuyuchoyu dlya nih i tomu dlya zabezpechennya tilesnoyi cilisnosti ta dobrobutu interseks lyudej v razi neobhidni maye buti dostupnoyu psihosocialna pidtrimka Genetichnij vidbir Etika preimplantacijnoyi genetichnoyi diagnostiki dlya poperedzhennya narodzhennya ditini z interseksnimi oznakami bula predmetom 11 statej u vipusku American Journal of Bioethics za zhovten 2013 roku 74 Shiroko poshireni dokazi pererivannya vagitnosti vnaslidok prenatalnogo testuvannya a takozh prenatalnogo likuvannya gormonami dlya zapobigannya rozvitku interseksnih oznak 75 Medichne fotografuvannya Fotografiyi interseksnih dityachih genitalij rozpovsyudzhuyutsya v medichnih spilnotah z dokumentalnoyu metoyu a osobi z interseks risami mozhut prohoditi povtorni obstezhennya statevih organiv i demonstruvati yih medichnim brigadam Obgovoryuvalis problemi pov yazani z dosvidom medichnogo fotografuvannya interseks ditej 76 a takozh yihni etichni normi kontrol ta vikoristannya 77 78 Dosvid takogo fotografuvannya dlya bagatoh lyudej z interseksnimi risami suprovodzhuyetsya vidchuttyam bezsillya ta prinizhennya 78 Prichini RedaguvatiZigotna genetichno obumovlena interseksnist Redaguvati Ye rezultatom vidhilennya vid normi naboru statevih hromosom i geniv v moment zaplidnennya pri z yednanni gamet v zigotu Za harakterom porushennya buvaye triployidnoyu abo inshoyu aneuployidnoyu interseksnistyu Diployidna interseksnist sposterigayetsya pri shreshuvanni riznih geografichnih ras u metelika neparnogo shovkopryada prichomu abo u samok abo u samciv v zalezhnosti vid tipu shreshuvannya Interseksnist u lyudini takozh mozhe buti viklikana porushennyam normalnogo chisla statevih hromosom Pri comu u muh drozofil viznachalnim u rozvitku stati ye spivvidnoshennya chisla par statevih hromosom i autosom tomu u nih interseksnist zvichajno pov yazana z porushennyam cogo spivvidnoshennya napriklad sposterigayetsya pri spivvidnoshenni 3A 2X tri nabori autosom na dvi statevi hromosomi U lyudini viznachalnim chinnikom rozvitku cholovichoyi stati ye nayavnist Y hromosomi pri comu risi interseksnosti sposterigayutsya u cholovikiv z sindromom Klajnfeltera nabir statevih hromosom XXY Gormonna interseksnist Redaguvati Yaksho u tvarin za vidilennyam statevimi zalozami cholovichih chi zhinochih gormoniv viznachayut rozvitok vtorinnih statevih oznak to u nih mozhna sposterigati yavishe gormonalnoyi interseksnosti Yaksho taku tvarinu kastruvati i zrobiti peresadku statevoyi zalozi inshoyi stati vidbuvayetsya maskulinizaciya abo vidpovidno feminizaciya organizm staye interseksnim Pri parazitarnij kastraciyi u rakopodibnih napriklad sprichinenoyi parazitichnim rachkom sakkulina vidbuvayutsya shozhi yavisha Interseks ta prava lyudini Redaguvati nbsp Gonkongska interseks aktivistka Smol LyukInterseks lyudi stikayutsya iz stigmatizaciyeyu ta diskriminaciyeyu vid narodzhennya osoblivo koli interseks variaciya ye pomitnoyu U deyakih krayinah osoblivo v Africi ta Aziyi zustrichayetsya navit ditovbivstvo ta stigmatizaciya simej Materiv u Shidnij Africi mozhut zvinuvatiti u chaklunstvi a narodzhennya interseksnoyi ditini mozhut opisati yak proklyattya 79 80 81 Interseksni nemovlyata ta diti taki yak diti z neodnoznachnimi zovnishnimi statevimi organami mozhut buti hirurgichno ta abo gormonalno zmineni shob vidpovidati prijnyatnim statevim harakteristikam 82 Taki proceduri mozhut peredbachati takozh sterilizaciyu Dorosli v tomu chisli elitni sportsmen k i takozh buli predmetami takogo likuvannya 83 84 Ci zayavi vse chastishe viznayutsya porushennyami prav lyudini iz zayavami agentstv OON 85 67 parlamentu Avstraliyi 65 a takozh nimeckih ta shvejcarskih etichnih institutiv 66 Organizaciyi interseks lyudej takozh vipuskali spilni zayavi protyagom dekilkoh rokiv vklyuchayuchi deklaraciyu Malti tretogo Mizhnarodnogo forumu interseks lyudej Doslidzhennya vkazuyut na zrostannya konsensusu shodo togo sho riznobichni interseksni tila ye normalnimi prote porivnyano ridkisnimi formami lyudskoyi biologiyi 86 a pravozahisni ustanovi posilyuyut kontrol za medichnoyu praktikoyu ta problemami diskriminaciyi interseksnih lyudej V rezultati pershogo mizhnarodnogo pilotnogo doslidzhennya 2013 roku Prava lyudini mizh stat i Dan Kristian Gattas Dan Christian Ghattas 62 87 viyaviv sho interseksni lyudi piddayutsya diskriminaciyi u vsomu sviti Rada Yevropi vidilyaye kilka problemnih oblastej Rivne pravo na zhittya ta profilaktiku medichnih procedur bez usvidomlenoyi zgodi vklyuchayuchi likuvannya yake vvazhayetsya nepotribnim Vidalennya interseksu yak vilikovnogo medichnogo stanu ale takogo sho mozhe prohoditi medichne likuvannya za usvidomlenoyu zgodoyu Rivne stavlennya za zakonom vklyuchayuchi konkretni pravovi polozhennya podibni do inshih ohoplenih klasiv Dostup do informaciyi medichnih kartok konsultacij ta pidtrimki Samoviznachennya u viznanni stati shlyahom shvidkogo dostupu do oficijnih dokumentiv 64 Vprovadzhennya zahistu prav lyudini v zakonodavstvo ta regulyuvannya progresuvalo povilno U 2011 roci Kristian Felling Christiane Volling vigrala pershu uspishnu spravu proti hirurga za hirurgichne vtruchannya bez zgodi 88 U 2015 roci Rada Yevropi vpershe viznala pravo interseksnih osib ne prohoditi likuvannya za priznachennyam stati 64 U kvitni 2015 roku Malta stala pershoyu krayinoyu yaka zaboronila nesamoviti medichni vtruchannya z metoyu modifikaciyi statevoyi anatomiyi v tomu chisli interseksnih lyudej 68 89 V ostanni roki prava interseks lyudej stali predmetom dopovidej kilkoh nacionalnih ta mizhnarodnih ustanov zokrema Shvejcarskoyi nacionalnoyi konsultativnoyi komisiyi z biomedichnoyi etiki 2012 r 66 specialnogo dopovidacha OON z pitan katuvan ta inshih zhorstokih nelyudskih abo takih sho prinizhuyut gidnist povodzhen abo pokaran 2013 r 67 ta senatu Avstraliyi 2013 r 65 2015 roku do nih priyednalisya Rada Yevropi Upravlinnya Verhovnogo komisara OON z prav lyudini ta Vsesvitnya organizaciya ohoroni zdorov ya U kvitni 2015 roku Malta stala pershoyu krayinoyu yaka zaboronila primusovi medichni vtruchannya 89 68 zgidno iz Zakonom pro gendernu identichnist ta virazhennya stati 89 68 U tomu zh roci Rada Yevropi stala pershoyu ustanovoyu yaka zayavila sho interseks lyudi mayut pravo ne prohoditi korekciyu stati 64 2017 roku neuryadovi pravozahisni organizaciyi Amnesty International 90 91 ta Human Rights Watch 92 93 94 opublikuvali zviti pro prava interseks ditej U sichni 2016 roku Ministerstvo ohoroni zdorov ya Chili nakazalo prizupiniti nepotribne normalizacijne likuvannya dlya interseksnih ditej vklyuchno z operaciyami sho mayut nezvorotni naslidki do dosyagnennya nimi viku koli voni zmozhut prijmati rishennya samostijno 95 96 97 98 99 Zahist vid diskriminaciyi Redaguvati nbsp Zahist za oznakami stati Zahist na osnovi interseks statusu Zahist za oznakami interseksu v mezhah oznaki statiNa sogodni kilka yurisdikcij zabezpechuyut zahist vid diskriminaciyi dlya interseks lyudej Pivdenno Afrikanska Respublika bula pershoyu krayinoyu yaka dodala interseks do zakonodavstva yak chastinu oznaki stat 100 Avstraliya bula pershoyu krayinoyu yaka dodala nezalezhnij atribut interseksnij status 101 Malta bula pershoyu hto prijnyav bilsh shiroki ramki statevih oznak cherez zakonodavstvo yake takozh pripinilo zmini statevih oznak nepovnolitnih zdijsneni z socialnih ta kulturnih prichin 69 U Bosnii i Gercegovini viznacheno yak statevi oznaki 102 103 Greciya zaboronyaye diskriminaciyu ta zlochini na grunti nenavisti na osnovi statevih oznak z 24 grudnya 2015 roku 104 105 Pracevlashtuvannya Redaguvati Avstralijske opituvannya 2015 roku sered lyudej yaki narodilisya z netipovimi statevimi oznakami viyavilo visokij riven bidnosti krim duzhe visokogo rivnya dostrokovogo zalishennya shkoli ta vishogo za serednij riven invalidnosti 106 U posibniku robotodavciv shodo interseksnoyi inklyuziyi opublikovanomu Pride in Diversity ta organizaciyeyu Intersex International Australia takozh rozkrivayutsya vipadki diskriminaciyi pri pracevlashtuvanni 107 Ohorona zdorov ya Redaguvati Zahist vid diskriminaciyi peretinayetsya z primusovim likuvannyam Maltijskij zahist za statevimi oznakami zabezpechuye chitkij zahist vid nepotribnih ta shkidlivih modifikacij statevih oznak ditej 68 69 U travni 2016 roku Ministerstvo ohoroni zdorov ya ta socialnih sluzhb SShA opublikuvalo zayavu v yakij roz yasnyuvalo Rozdil 1557 Zakonu pro dostupnu medichnu dopomogu v yakomu zaznachayetsya sho Zakon zaboronyaye diskriminaciyu za nayavnistyu interseksnih oznak abo netipovih statevih oznak u derzhavnomu finansuvanni ohoroni zdorov ya yak chastinu zaboroni diskriminaciyi za oznakoyu stati 108 Sport Redaguvati U 2013 roci v medichnomu zhurnali bulo rozkrito sho chotiri nenazvani elitni sportsmenki z krayin sho rozvivayutsya buli piddani gonadektomiyi sterilizaciya ta chastkovij klitoridektomiyi kalictvo zhinochih statevih organiv pislya togo yak testuvannya testosteronu pokazalo sho voni mayut interseksnij stan Testuvannya na testosteron bulo zaprovadzheno vnaslidok spravi Kaster Semenya pivdennoafrikanskoyi bigunki yaka projshla testuvannya zavdyaki svoyij zovnishnosti 109 110 111 112 Nemaye dokaziv togo sho vrodzhena giperandrogeniya u zhinok sportsmenok nadaye perevagu v sporti 113 114 Div takozh RedaguvatiInterseksizm Psevdogermafroditizm Spravzhnij germafroditizm Prava interseks lyudejPosilannya RedaguvatiIstoriyi interseks lyudej Arhivovano 9 veresnya 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Arnold Arthur P 24 travnya 2005 Sexually dimorphic expression of trkB a Z linked gene in early posthatch zebra finch brain Proceedings of the National Academy of Sciences of the United States of America 102 21 s 7730 7735 ISSN 0027 8424 PMC 1140405 PMID 15894627 doi 10 1073 pnas 0408350102 Arhiv originalu za 20 bereznya 2021 Procitovano 23 grudnya 2020 Suzuki Yuya Kuramitsu Kazumu Yokoi Tomoyuki 14 chervnya 2019 Morphology and sex specific behavior of a gynandromorphic Myrmarachne formicaria Araneae Salticidae spider Die Naturwissenschaften 106 7 8 s 34 ISSN 1432 1904 PMID 31201570 doi 10 1007 s00114 019 1625 x Arhiv originalu za 27 lyutogo 2021 Procitovano 23 grudnya 2020 Half male half female butterfly steals the show at Natural History Museum the Guardian angl 11 lipnya 2011 Arhiv originalu za 12 listopada 2020 Procitovano 23 grudnya 2020 a b 5 mifiv pro interseks lyudej yaki chas zrujnuvati Amnesty International Ukraine ukr 7 listopada 2019 Arhiv originalu za 24 zhovtnya 2020 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grudnya 2020 rekomenduyetsya displayauthors dovidka Mouriquand Pierre D E Gorduza Daniela Brindusa Gay Claire Lise Meyer Bahlburg Heino F L Baker Linda Baskin Laurence S Bouvattier Claire Braga Luis H ta in 2016 06 Surgery in disorders of sex development DSD with a gender issue If why when and how Journal of Pediatric Urology angl 12 3 s 139 149 doi 10 1016 j jpurol 2016 04 001 Arhiv originalu za 8 bereznya 2021 Procitovano 27 grudnya 2020 rekomenduyetsya displayauthors dovidka Creighton Sarah M Michala Lina Mushtaq Imran Yaron Michal 2 sichnya 2014 Childhood surgery for ambiguous genitalia glimpses of practice changes or more of the same Psychology amp Sexuality angl 5 1 s 34 43 ISSN 1941 9899 doi 10 1080 19419899 2013 831214 Arhiv originalu za 11 travnya 2021 Procitovano 27 grudnya 2020 UN Committee against Torture UN Committee on the Rights of the Child UN Committee on the Rights of People with Disabilities UN Subcommittee on Prevention of Torture and other Cruel Inhuman or Degrading Treatment or Punishment Juan Mendez Dainius Pῡras Dubravka Simonoviae Marta Santos Pais ta in 24 zhovtnya 2016 Intersex Awareness Day Wednesday 26 October End violence and harmful medical practices on intersex children and adults UN and regional experts urge Office of the High Commissioner for Human Rights Arhiv originalu za 21 listopada 2016 rekomenduyetsya displayauthors dovidka a b Ghattas Dan Christian Fond Gajnriha Bellya September 2013 Human Rights Between the Sexes Arhiv originalu za 23 veresnya 2015 Procitovano 27 grudnya 2020 Beyond the Boundary Knowing and Concerns Intersex October 2015 Intersex report from Hong Kong China and for the UN Committee Against Torture the Convention against Torture and Other Cruel Inhuman or Degrading Treatment or Punishment Arhiv originalu za 26 bereznya 2017 Procitovano 27 grudnya 2020 a b v g Council of Europe Commissioner for Human Rights April 2015 Human rights and intersex people Issue Paper Arhiv originalu za 6 sichnya 2016 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